DESMOPLASTIC TUMOR OF SMALL ROUND CELLS IN THE ABDOMINAL REGION IN YOUNG PATIENT: CASE REPORT
DOI:
https://doi.org/10.47820/recima21.v2i11.962Keywords:
desmoplastic small round cell tumor, peritoneum, neoplasmsAbstract
Introduction: The small round cell desmoplastic tumor is a rare and very aggressive disease. It predominates in adolescents and young adults.The prognosis is usually very bad. Objective: Report a case of desmoplastic small round cell tumor in a 19-year-old male patient. Materials and methods: Data obtained through a review of the patient's medical record, complementary exams and literature review. Case report: Patient with a clinical condition of consumption and abdominal masses. On physical exam exhibits a palpable abdominal mass in the hypogastric region. The diagnosis was confirmed by immunohistochemistry. The proposed therapy was the protocol for Ewing's sarcoma (first-line regimen). However, the patient had disease progression despite fourth-line treatment. He refused exclusive palliative treatment. Despite the treatments performed, the patient died in April 2021. Discussion: TDCR is a highly progressive type of neoplasm that is histologically constituted by small undifferentiated cells. Symptoms are associated with masses that can metastasize to other organs. The body responded with partial remission to chemotherapy regimens, sending it forward for the disease to advance rapidly, with fatal consequences. Conclusion: Due to its rarity, diagnosis and treatment are a challenge, and, for this reason, the study of this pathology becomes extremely important.
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