TRAINING OF STRENGTH AND MUSCULAR MUSCULAR RESISTANCE IN DUCHENNE MUSCULAR DYSTROPHY: LITERATURE NARRATIVE REVIEW

Abstract

Duchenne muscular dystrophy (DMD) is a hereditary progressive disease that causes musculoskeletal degradation due to lack and/or decrease of dystrophin protein, due to deficiency of the DMD gene located in the Xp21 region presenting the first signs between the third and fifth year of life with progressive muscle weakening, evolving to the respiratory musculature and cardiac failure. In this context, physiotherapy minimizes musculoskeletal impairment, assists in the maintenance of cardiovascular and respiratory functions and, together with early respiratory muscle training (MRT), assists in increasing respiratory strength and endurance. Therefore, the aim of this study was to discuss DMD and the effects of MRT with a focus on the use of the PowerBreathe ® (PB) device, in addition to enriching the literature related to the theme, through a narrative review of the literature. The review was made in the scientific databases Scielo, Pubmed, Lilacs, VHL and Google Scholar using descriptors: Duchenne muscular dystrophy, PowerBreathe®, Threshold® IMT, respiratory muscle training and endurance in portuguese and endurance between 2001 and 2019. This review showed the effectiveness of physiotherapy in patients with DMD and early treatment, which aims to maintain motor and respiratory function; and that the most commonly used equipment for TMR in general is Threshold® IMT. In addition, it points to the scarcity of specific studies on the use of CP in DMD; suggesting more research that can elucidate the direct benefits of this device to patients with DMD.