EFFECTIVENESS OF RESPIRATORY MUSCLE STRENGTH AND ENDURANCE TRAINING IN KARTAGENER SYNDROME: CASE REPORT

Abstract

Kartagener Syndrome (KS) is a rare autosomal recessive disease that is characterized by chronic sinusitis, bronchiectasis and situs inversus. There is modification of dynein, a protein that couples to microtubules, responsible for the frequency of ciliary beats, in the bronchial epithelium, making them immobile, compromising mucociliary clearance in the respiratory tract. As a consequence, must present repeated infections of the upper and lower airways since childhood, and usually bronchitis, pneumonia, hemoptysis, otitis media, sinusitis, among others. In this context, it is believed that these requirements may lead to respiratory muscle weakness. Thus, the study hypothesis was that respiratory physiotherapy associated with respiratory muscle training (RMT) and physical training (RT) promotes improvement in respiratory muscle strength and endurance, as well as in cardiorespiratory conditioning and functional capacity. A 28-year-old Caucasian male, 94 kg, 1.74 m, with BMI = 31.05 kg / m2, who underwent RMR associated with physical conditioning, was eligible. It is known that many studies are found in the scientific literature prove the TMR benefits, regardless of whether or not there is an installed disease; this case study is pioneering regarding the use of Power Breathe (PB) in this population. According to the present study, it is necessary that TMR associated with TF brings improvement to the individual in terms of respiratory muscle strength and endurance, cardiorespiratory conditioning and functional capacity. However, reports in the scientific literature on the subject, as well as on the more detailed prognosis, are still scarce and there are no specifically randomized studies improvement.